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Pediatric Dialysis pp 585–593Cite as

Dialytic management of inborn errors of metabolism

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Abstract

Metabolic crises in children with inborn errors of metabolism are caused by the accumulation of neurotoxic metabolites. Rapid elimination of these metabolites is crucial to prevent irreversible neuronal damage since long-term outcome is correlated with the duration of the metabolic crisis. This chapter reviews the principles of dietetic, pharmacological and dialytic management of neonatal metabolic emergencies.

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Authors
  1. F. S. Schaefer
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  2. M. Daschner
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Editor information

Editors and Affiliations

  1. Children’s Mercy Hospital, University of Missouri, Kansas City School of Medicine, Kansas City, MO, USA

    Bradley A. Warady

  2. University Children’s Hospital, Heidelberg, Germany

    Franz S. Schaefer

  3. Health Science Center, State University of New York at Stony Brook, Stony Brook, NY, USA

    Richard N. Fine

  4. Lucille Packard Children’s Hospital at Stanford, Stanford University, School of Medicine, Stanford, CA, USA

    Steven R. Alexander

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© 2004 Springer Science+Business Media Dordrecht

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Schaefer, F.S., Daschner, M. (2004). Dialytic management of inborn errors of metabolism. In: Warady, B.A., Schaefer, F.S., Fine, R.N., Alexander, S.R. (eds) Pediatric Dialysis. Springer, Dordrecht. https://doi.org/10.1007/978-94-007-1031-3_35

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  • DOI: https://doi.org/10.1007/978-94-007-1031-3_35

  • Publisher Name: Springer, Dordrecht

  • Print ISBN: 978-94-010-3770-9

  • Online ISBN: 978-94-007-1031-3

  • eBook Packages: Springer Book Archive

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