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Valve Disease

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Sudden Cardiac Death in the Young and Athletes

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Abstract

SCD may occur in young people affected by congenital valve aortic stenosis, whether unicuspid or bicuspid with dysplastic cusps [1] (Figs. 6.1, and 6.2). At a young age, the cusps rarely present with a dystrophic calcification, a phenomenon which usually occurs in adult or in the elderly [2–4]. When it happens prematurely, it is usually secondary to endocarditis (Fig. 6.3). SCD is arrhythmic and the arrhythmogenic substrate consists of left ventricular hypertrophy and subendocardial ischemia, in terms of myocytolisis and replacement-type fibrosis [1, 5].

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Authors and Affiliations

  1. Cardiovascular Pathology Department of Cardiac, Thoracic and Vascular Sciences, University of Padua, Padova, Italy

    Gaetano Thiene & Cristina Basso

  2. Cardiology Department of Cardiac, Thoracic and Vascular Sciences, University of Padua, Padova, Italy

    Domenico Corrado

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  1. Gaetano Thiene
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  2. Domenico Corrado
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  3. Cristina Basso
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© 2016 Springer-Verlag Milan

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Thiene, G., Corrado, D., Basso, C. (2016). Valve Disease. In: Sudden Cardiac Death in the Young and Athletes. Springer, Milano. https://doi.org/10.1007/978-88-470-5776-0_6

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  • DOI: https://doi.org/10.1007/978-88-470-5776-0_6

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  • Publisher Name: Springer, Milano

  • Print ISBN: 978-88-470-5775-3

  • Online ISBN: 978-88-470-5776-0

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