Ebstein’s Anomaly and Arrhythmia Management

  • Sara Foresti
  • Pierpaolo Lupo
  • Riccardo CappatoEmail author


Arrhythmias represent a major issue in patients with Ebstein’s anomaly (EA). In these patients, congenital and acquired substrates for arrhythmias coexist and can manifest at different stages of the disease.

Atrioventricular reentrant tachycardia related to accessory pathways can occur in children with EA. In adolescents and adults, arrhythmia symptoms are the most common presentation of EA with accessory pathway or nodal atrioventricoular reentrant tachycardia being more common at a younger age, whereas later in life, atrial tachycardia and atrial fibrillation have a higher prevalence.

Technical improvements and a better understanding of arrhythmia substrate in these patients have increased transcatheter and surgical ablation success rates, and these strategies should be applied aggressively to treat arrhythmias.


Atrial Fibrillation Congenital Heart Disease Tricuspid Valve Atrial Tachycardia Accessory Pathway 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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Copyright information

© Springer-Verlag Italia 2014

Authors and Affiliations

  • Sara Foresti
    • 1
  • Pierpaolo Lupo
    • 1
  • Riccardo Cappato
    • 1
    Email author
  1. 1.Center of Clinical Arrhythmia and Electrophysiology, IRCCS Policlinico San DonatoSan Donato Milanese, MilanItaly

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