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Congenital Cystic Adenomatoid Malformations

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Pediatric Thoracic Surgery

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Abstract

Congenital cystic adenomatoid malformations (CCAMs) are relatively rare disturbances of lung development in which part of the parenchyme is replaced by hamartomatous cysts of different sizes lined by a respiratory epithelium that may communicate indirectly with the airway. It occurs in about 1 in 30,000 gestations and is slightly more frequent in males [1]. CCAMs account for infectious complications later in life and can: interfere with the lung development and physiology of the fetus; cause neonatal respiratory distress; be associated with some tumors. The origin of CCAMs is not well known, their behavior is unpredictable, and their treatment controversial. These aspects will be addressed in this chapter.

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  1. Pediatric Surgery, Hospital Universitario La Paz, Madrid, Spain

    Juan A. Tovar

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Correspondence to Juan A. Tovar .

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  1. Pediatric Surgery, University of Bologna, Bologna, Italy

    Mario Lima

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Tovar, J.A. (2013). Congenital Cystic Adenomatoid Malformations. In: Lima, M. (eds) Pediatric Thoracic Surgery. Springer, Milano. https://doi.org/10.1007/978-88-470-5202-4_21

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  • DOI: https://doi.org/10.1007/978-88-470-5202-4_21

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