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Congenital Immunodeficiencies

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Neonatology

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Abstract

The primary immunodeficiency diseases (PIDs) are a heterogeneous group of inherited disorders with defects in one or more components of the immune system. PIDs are classified into T lymphocyte, B lymphocyte, phagocytic cell, and complement deficiencies. This classification is simple and practical because clinical symptoms, mainly susceptibility to infections, vary according to the affected arm of the immune system. The prognosis of these disorders and their treatment depends on their early recognition and initiation of appropriate management.

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Author information

Authors and Affiliations

  1. Department of Pediatrics, Spedali Civili Hospital, Italy

    Alessandro Plebani

  2. University of Brescia, Brescia, Italy

    Alessandro Plebani

Authors
  1. Alessandro Plebani
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  2. Gaetano Chirico
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Editor information

Editors and Affiliations

  1. Department of Pediatrics, Obstetrics and Reproductive Medicine, Division of Neonatology, University of Siena General Hospital S. Maria alle Scotte Azienda Ospedaliera Universitaria Senese, Siena, Italy

    Giuseppe Buonocore (Professor of Pediatrics and Neonatology, Head of School of Pediatrics) (Professor of Pediatrics and Neonatology, Head of School of Pediatrics)

  2. University of Siena, Siena, Italy

    Rodolfo Bracci (Formerly Professor of Pediatrics and Head of Department of Pediatrics, Obstetrics and Reproductive Medicine) (Formerly Professor of Pediatrics and Head of Department of Pediatrics, Obstetrics and Reproductive Medicine)

  3. University of Liverpool, UK

    Michael Weindling (Professor of Perinatal Medicine, Director of Postgraduate Research, Head of School of Paediatrics Mersey Deanery) (Professor of Perinatal Medicine, Director of Postgraduate Research, Head of School of Paediatrics Mersey Deanery)

  4. Department of Women’s and Children’s Health, Institute of Translational Medicine, Liverpool, UK

    Michael Weindling (Professor of Perinatal Medicine, Director of Postgraduate Research, Head of School of Paediatrics Mersey Deanery) (Professor of Perinatal Medicine, Director of Postgraduate Research, Head of School of Paediatrics Mersey Deanery)

  5. Liverpool Women’s Hospital, Liverpool, UK

    Michael Weindling (Professor of Perinatal Medicine, Director of Postgraduate Research, Head of School of Paediatrics Mersey Deanery) (Professor of Perinatal Medicine, Director of Postgraduate Research, Head of School of Paediatrics Mersey Deanery)

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© 2012 Springer-Verlag Italia

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Plebani, A., Chirico, G. (2012). Congenital Immunodeficiencies. In: Buonocore, G., Bracci, R., Weindling, M. (eds) Neonatology. Springer, Milano. https://doi.org/10.1007/978-88-470-1405-3_109

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  • DOI: https://doi.org/10.1007/978-88-470-1405-3_109

  • Publisher Name: Springer, Milano

  • Print ISBN: 978-88-470-1404-6

  • Online ISBN: 978-88-470-1405-3

  • eBook Packages: MedicineMedicine (R0)

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