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Pulmonary atresia with ventricular septal defect

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Congenital Heart Defects

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Abstract

Pulmonary atresia with ventricular septal defect is a rare malformation, with an incidence of 0.042–0.070 per 1000 live births, or 1.5–3.4% of congenital heart defects, and a slightly higher prevalence in males than in females. Eighteen to 20% of patients with tetralogy of Fallot have pulmonary atresia.

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Authors and Affiliations

  1. Department of Cardiovascular Surgery, Centre Hospitalier Universitaire Vaudois (CHUV), 46, rue du Bugnon, CH-1011, Lausanne, Switzerland

    Antonio F. Corno MD, FRCS, FETCS

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  1. Antonio F. Corno MD, FRCS, FETCS
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© 2004 Springer-Verlag Berlin Heidelberg

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Corno, A.F. (2004). Pulmonary atresia with ventricular septal defect. In: Congenital Heart Defects. Steinkopff, Heidelberg. https://doi.org/10.1007/978-3-7985-1934-3_4

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  • DOI: https://doi.org/10.1007/978-3-7985-1934-3_4

  • Publisher Name: Steinkopff, Heidelberg

  • Print ISBN: 978-3-642-62158-1

  • Online ISBN: 978-3-7985-1934-3

  • eBook Packages: Springer Book Archive

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