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Eyelid motor abnormalities in progressive supranuclear palsy

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Progressive Supranuclear Palsy: Diagnosis, Pathology, and Therapy

Part of the book series: Journal of Neural Transmission. Supplementa ((NEURAL SUPPL,volume 42))

Summary

Eyelid motor abnormalities found in progressive supranuclear palsy are reviewed. Electrophysiological correlates of blepharospasm, levator inhibition (blepharokolysis) and supranuclear paralysis of lid closure are presented.

Disorders of eyelid motility are not uncommon in progressive supranuclear palsy (PSP). They may be found in about one third of patients with this syndrome (Jackson et al., 1983; Golbe et al., 1989). This is not surprising since ocular and eyelid movements are highly coordinated, mainly in the vertical plane (Gordon, 1951; Kennard and Smith, 1963; Kennard and Glaser, 1964), and a supranuclear ophthalmoplegia with down gaze impairment is a cardinal feature of PSP (Steele et al., 1964). The spectrum of eyelid motor disorders described in PSP includes blinking abnormalities, lid retraction, blepharospasm, levator inhibition and supranuclear palsy of eye closure.

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Author information

Authors and Affiliations

  1. Servicio de Neurologia, Hospital General “Gregorio Marañón”, Doctor Esquerdo, 46, E-28007, Madrid, Spain

    Dr. F. Grandas

  2. Sección de Neurofisiología, Hospital General “Gregorio Marañón”, Madrid, Spain

    A. Esteban

Authors
  1. Dr. F. Grandas
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  2. A. Esteban
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Editor information

Editors and Affiliations

  1. Neurology Service, Hospital Clinic, Faculty of Medicine, University of Barcelona, Spain

    E. Tolosa

  2. Neurology Service, Robert Wood Johnson University Hospital, New Brunswick, NJ, USA

    R. Duvoisin

  3. Neurological Tissue Bank, Faculty of Medicine, University of Barcelona, Spain

    F. F. Cruz-Sánchez

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© 1994 Springer-Verlag Wien

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Grandas, F., Esteban, A. (1994). Eyelid motor abnormalities in progressive supranuclear palsy. In: Tolosa, E., Duvoisin, R., Cruz-Sánchez, F.F. (eds) Progressive Supranuclear Palsy: Diagnosis, Pathology, and Therapy. Journal of Neural Transmission. Supplementa, vol 42. Springer, Vienna. https://doi.org/10.1007/978-3-7091-6641-3_3

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  • DOI: https://doi.org/10.1007/978-3-7091-6641-3_3

  • Publisher Name: Springer, Vienna

  • Print ISBN: 978-3-211-82541-9

  • Online ISBN: 978-3-7091-6641-3

  • eBook Packages: Springer Book Archive

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