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Clinical Diagnostic Criteria

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Multiple System Atrophy

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Abstract

The diagnosis of MSA represents a major challenge in movement disorders clinics. In early disease stages, the parkinsonian variant of MSA (MSA-P) may be indistinguishable from idiopathic PD, whereas in more advanced stages, features overlapping with the clinical presentation of progressive supranuclear palsy (PSP) or dementia with Lewy bodies (DLB) may be also present in MSA. Also, inherited (like late onset atypical Friedreich’s ataxia, spinocerebellar ataxias 2,3 or 6 without an obvious family history) or acquired causes of late-onset cerebellar ataxia need to be ruled out to diagnose cerebellar MSA (MSA-C).

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Authors and Affiliations

  1. Department of Neuroscience, Mental Health and Sensory Organs, “Sapienza” University of Rome, Rome, Italy

    Alessandra Fanciulli MD

  2. Division of Neurobiology, Department of Neurology, Innsbruck Medical University, Anichstrasse 35, Innsbruck, 6020, Austria

    Alessandra Fanciulli MD & Gregor K. Wenning MD, PhD, MSC

Authors
  1. Alessandra Fanciulli MD
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  2. Gregor K. Wenning MD, PhD, MSC
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Correspondence to Alessandra Fanciulli MD .

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Editors and Affiliations

  1. Division of Clinical Neurobiology, Innsbruck Medical University, Innsbruck, Austria

    Gregor K. Wenning

  2. Department of Neurology Division of Neurobiology, Innsbruck Medical University, Innsbruck, Austria

    Alessandra Fanciulli

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© 2014 Springer-Verlag Wien

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Fanciulli, A., Wenning, G.K. (2014). Clinical Diagnostic Criteria. In: Wenning, G., Fanciulli, A. (eds) Multiple System Atrophy. Springer, Vienna. https://doi.org/10.1007/978-3-7091-0687-7_7

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  • DOI: https://doi.org/10.1007/978-3-7091-0687-7_7

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  • Online ISBN: 978-3-7091-0687-7

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