Skip to main content
  • 1456 Accesses


Kutane Lymphome zählen zu den extranodalen Non-Hodgkin-Lymphomen und sind eine heterogene Gruppe lymphoproliferativer Erkrankungen der Haut mit sehr unterschiedlicher klinischer Symptomatik und Prognose. Die Hälfte aller primären kutanen Lymphome manifestiert sich als Mycosis fungoides, ein T-Zell-Lymphom niedrigen Malignitätsgrades. Beim Sézary-Syndrom handelt es sich um ein kutanes T-Zell-Lymphom mit leukämischer Ausschwemmung atypischer T-Zellen. Die lymphomatoide Papulose ist ein seltenes, kutanes, niedrig-malignes T-Zell-Lymphom, das alle Altersklassen betreffen kann. Primär kutane B-Zell-Lymphome sind seltener als kutane T-Zell-Lymphome und machen nur etwa 20–25 % aller kutanen Lymphome aus. Hier unterscheidet man indolente Formen wie das follikuläre Keimzentrumslymphom und das Marginalzonenlymphom von aggressiven B-Zell- Lymphomen, wie dem primär kutanen diffus großzelligen B-Zell-Lymphom vom Beintyp.

This is a preview of subscription content, log in via an institution to check access.

Access this chapter

Subscribe and save

Springer+ Basic
EUR 32.99 /Month
  • Get 10 units per month
  • Download Article/Chapter or Ebook
  • 1 Unit = 1 Article or 1 Chapter
  • Cancel anytime
Subscribe now

Buy Now

USD 29.95
Price excludes VAT (USA)
  • Available as PDF
  • Read on any device
  • Instant download
  • Own it forever
USD 69.99
Price excludes VAT (USA)
  • Available as EPUB and PDF
  • Read on any device
  • Instant download
  • Own it forever
Hardcover Book
USD 89.99
Price excludes VAT (USA)
  • Durable hardcover edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Purchases are for personal use only

Institutional subscriptions

Similar content being viewed by others

Weiterführende Literatur

  • Dippel E, Assaf C, Becker JC, et al. (Hrsg) S2k – Kurzleitlinie – Kutane Lymphome (ICD10 C82–C86) Update 2016.–027l_S2k_Kutane_Lymphome_2017–10.pdf

  • Golling P, Cozzio A, Dummer R, French L, Kempf W (2008) Primary cutaneous B-cell lymphomas – clinicopathological, prognostic and therapeutic characterisation of 54 cases according to the WHO-EORTC classification and the ISCL/EORTC TNM classification system for primary cutaneous lymphomas other than mycosis fungoides and Sezzary-Syndrome. Leuk Lymphoma 49: 1094–1103

    Google Scholar 

  • Mangold AR, Thompson A, Davis MD, et al. (2018) Early clinical manifestations of Sézary-Syndrome: A Multicenter Retrospective Cohort Study. J Am Acad Dermatol 77: 719–727. doi: 10.1016/j.jaad.2017.05.036

  • National Comprehensive Cancer Network (NCCN) (Hrsg) Guidelines n-HsLV. (Zugegriffen: 08.05.2018)

  • Nicolay JP, Wobser M. Cutaneous B (2016) -cell lymphomas – pathogenesis, diagnostic workup, and therapy. J Dtsch Dermatol Ges 14: 1207–1224

    Google Scholar 

  • Olsen E, Vonderheid E, Pimpinelli N, et al. (2007) Revisions to the staging and classification of mycosis fungoides and Sezzary-Syndrome: a proposal of the International Society for Cutaneous Lymphomas (ISCL) and the cutaneous lymphoma task force of the European Organization of Research and Treatment of Cancer (EORTC). Blood 110: 1713–1722

    Google Scholar 

  • Scarisbrick JJ, Prince HM, Vermeer MH, et al. (2015) Cutaneous Lymphoma International Consortium Study of Outcome in Advanced Stages of Mycosis Fungoides and Sezzary-Syndrome: Effect of Specific Prognostic Markers on Survival and Development of a Prognostic Model. J Clin Oncol 33: 3766–3773

    Google Scholar 

  • Senff NJ, Noordijk EM, Kim YH, et al. (2008) European Organization for Research and Treatment of Cancer and International Society for Cutaneous Lymphoma consensus recommendations for the management of cutaneous B-cell lymphomas. Blood 112: 1600–1609

    Google Scholar 

  • Suarez AL, Pulitzer M, Horwitz S, Moskowitz A, Querfeld C, Myskowski PL (2013) Primary cutaneous B-cell lymphomas: part I. Clinical features, diagnosis, and classification. J Am Acad Dermatol 69: 329 e321–313; quiz 341–322

    Google Scholar 

  • Swerdlow SH, Campo E, Pileri SA, et al. (2016) The 2016 revision of the World Health Organization classification of lymphoid neoplasms. Blood 127: 2375–2390

    Google Scholar 

  • Trautinger F, Knobler R, Willemze R, et al. (2006) EORTC consensus recommendations for the treatment of mycosis fungoides/Sezzary-Syndrome. Eur J Cancer 42: 1014–1030

    Google Scholar 

  • Trautinger F, Eder J, Assaf C, et al. (2017) European Organisation for Research and Treatment of Cancer consensus recommendations for the treatment of mycosis fungoides/Sezzary-Syndrome – Update 2017. Eur J Cancer 77: 57–74

    Google Scholar 

  • Vonderheid EC, Bernengo MG, Burg G, et al. (2002) Update on erythrodermic cutaneous T-cell lymphoma: report of the International Society for Cutaneous Lymphomas. J Am Acad Dermatol 46: 95–106

    Google Scholar 

Download references


Editor information

Editors and Affiliations

Rights and permissions

Reprints and permissions

Copyright information

© 2019 Springer-Verlag GmbH Deutschland, ein Teil von Springer Nature

About this chapter

Cite this chapter

Roenneberg, S., Plötz, S.G., Hein, R., Ring, J. (2019). Kutane Lymphome. In: Plötz, S.G., Hein, R., Ring, J., Biedermann, T. (eds) Häufige Hauttumoren in der Praxis. Springer, Berlin, Heidelberg.

Download citation

  • DOI:

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-662-57370-9

  • Online ISBN: 978-3-662-57371-6

  • eBook Packages: Medicine (German Language)

Publish with us

Policies and ethics