Abstract
Duodenal neuroendocrine tumors (NETs) (also called carcinoid tumors) are rare, with an incidence in the population of approximately 1 per million. They may be found incidentally on endoscopy as a mass in the submucosa at endoscopy (Fig. 14.1), or they can produce hormones that cause clinical syndromes. These tumors can make somatostatin, vasoactive intestinal polypeptide (VIP), or more commonly, gastrin. When they make gastrin, it is called the Zollinger-Ellison syndrome (ZES). Duodenal NETs may be either benign or malignant, but even when malignant, they have a low malignant potential. In general, they have an excellent prognosis.
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Norton, J.A. (2017). Surgery for Duodenal and Gastric Neuroendocrine Tumors. In: Howe, J. (eds) Endocrine and Neuroendocrine Surgery. Springer Surgery Atlas Series. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-54067-1_14
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DOI: https://doi.org/10.1007/978-3-662-54067-1_14
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