Gastrointestinal Tumors in Children

  • Alan P. LaddEmail author
  • Jay L. Grosfeld


The presentation of a gastrointestinal tumor remains a rarity in the practice of surgery for children. Primary tumors of the gastrointestinal tract are estimated to compose less than 5 % of all pediatric neoplasms. Estimates as to the prevalence of primary gastrointestinal malignancies with the incorporation of gastrointestinal-associated lymphomas approach 1 % of all pediatric malignancies. Lymphomas compose roughly three-quarters of gastrointestinal-related malignancies. The clinical presentation of these tumors, which arise anywhere from the level of the esophagus to the rectum, is either incidental or based on symptoms related to the mass or mass-effect of the tumor. The majority of presenting symptoms includes abdominal pain and vomiting. The tumors of the gastrointestinal tract can best be categorized based on their cellular differentiation. By order of prevalence gastrointestinal-related malignancies are composed of lymphomas, sarcomas, carcinomas, neuroendocrine tumors, teratomas, and hyperplastic stromal tumors or polyps.


Lymphoma Gastrointestinal stromal tumor Leiomyosarcoma Colorectal carcinoma Neuroendocrine tumor Carcinoid tumor Teratoma Inflammatory myofibroblastic tumor Familial adenomatous polyposis Juvenile polyp Peutz-Jeghers syndrome 


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© Springer-Verlag Berlin Heidelberg 2016

Authors and Affiliations

  1. 1.Department of SurgeryIndiana University School of Medicine, Riley Hospital for Children at IU HealthIndianapolisUSA

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