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ISSVA Classification of Vascular Anomalies

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Congenital Vascular Malformations


Although the existence of vascular anomalies is far from a new discovery, misconceptions regarding diagnosis and management persist. Fundamental to clarifying this misinformation is a comprehension of the categorization of diagnoses. Throughout many years, classification schemas have evolved. Since the 1980s, resulting from Mulliken’s insight, it has been generally accepted that the partition of vascular anomalies into those that proliferate (“tumors”) and those that are developmental aberrations (vascular malformations) provides a functional taxonomic separation [1]. Although vascular anomalies represent a spectrum of disorders, with some overlap, this partitioning into two separate groups serves as a functional division and can assist in the overall management plan and realistic conversation with patients and their families.

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The author is grateful for the patients with vascular anomalies, their families, and colleagues who participate in the care of and research in this field.

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Correspondence to Francine Blei MD, MBA .

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Blei, F. (2017). ISSVA Classification of Vascular Anomalies. In: Kim, YW., Lee, BB., Yakes, W., Do, YS. (eds) Congenital Vascular Malformations. Springer, Berlin, Heidelberg.

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  • Print ISBN: 978-3-662-46708-4

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