Truncular Lymphatic Malformation (LM): Primary Lymphedema
Primary lymphedema is defined as edema caused by lymphatic dysplasia and/or dysfunction due to congenital [1, 2] or unknown factors. Primary lymphedema occurs in 1 of every 10,000 people in the general population . A recent study in the author’s clinic showed that primary lymphedema accounted ~27% of the 3252 lymphedema cases in the last 2 years in the author’s lymphology clinic in Shanghai Ninth People’s Hospital (unpublished data).
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