• Arnold P. OranjeEmail author
  • Dirk Van Gysel


Mastocytosis is a proliferative disease of mast cells. Mastocytosis belongs to the Orphan diseases and is listed as such in the Orphanet database. Treatment is not indicated in most cutaneous variants and noncomplicated cases without complaints and/or systemic involvement. In cases with complaints or suspicion of systemic involvement, multidisciplinary approach is indicated.


Mastocytosis Orphan disease Mastocytoma Cutaneous mastocytosis Diffuse cutaneous mastocytosis Systemic mastocytosis 


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Copyright information

© Springer-Verlag Berlin Heidelberg 2015

Authors and Affiliations

  1. 1.Department of DermatologyMaasstad Hospital RotterdamRotterdamThe Netherlands
  2. 2.Department of PediatricsERASMUS MCRotterdamThe Netherlands
  3. 3.Department of PediatricsO.L.Vrouw HospitalAalstBelgium

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