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Pelizaeus-Merzbacher Disease

  • Jacob Valk
  • Marjo S. van der Knaap

Abstract

Pelizaeus-Merzbacher disease (PMD) is a rare neurological disorder affecting the myelination of the CNS in children. The disease can be subdivided into three types: the classical type, the connatal type, and the transitional form.

Keywords

White Matter Myelin Sheath Subcortical White Matter Transitional Form Centrum Semiovale 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer-Verlag Berlin Heidelberg 1989

Authors and Affiliations

  • Jacob Valk
    • 1
  • Marjo S. van der Knaap
    • 2
  1. 1.Department of Diagnostic Radiology and NeuroradiologyFree University HospitalAmsterdamThe Netherlands
  2. 2.Department of Child NeurologyAcademic HospitalUtrechtThe Netherlands

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