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Pathologie pp 164-168 | Cite as

Übertragbare spongiforme Enzephalopathien

  • J. W. Boellaard

Zusammenfassung

Dieser Gruppe von Erkrankungen des ZNS, die bei Menschen und Haustieren vorkommen, ist eine ungewöhnlich lange Inkubationszeit und dann ein meist rascher tödlicher Verlauf gemeinsam. Die bekanntesten hierzu gehörigen Krankheiten, die im folgenden besprochen werden sollen, sind Kuru, die Jakob-Creutzfeldt-Erkrankung (CJD) und die Gerstmann-Sträussler-Scheinker-Krankheit (GSS) beim Menschen sowie Scrapie und die bovine spongiforme Enzephalopathie (BSE) bei Haustieren. BSE sowie weitere Formen dieser Krankheitsgruppe bei Tieren wie u. a. bei Nerzen (transmissible Mink Encephalopathy TME) u. a. werden auf Verfüttern von mit Scrapie infizierten Kadavern zurückgeführt. Sie sind unter den international tiblichen Abkürzungen aufgeftihrt in.

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Copyright information

© Springer-Verlag Berlin Heidelberg 1995

Authors and Affiliations

  • J. W. Boellaard

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