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Psychological Profile and Behavioral Characteristics in the Prader-Willi Syndrome

  • L. M. G. Curfs
Part of the NATO ASI Series book series (volume 61)

Abstract

The Prader-Willi Syndrome is characterized by a number of clinical features including hypotonia, hyperphagia with childhood-onset obesity, hypogonadism, craniofacial abnormalities, a typical fat distribution and finely shaped hands and feet (Prader et al 1956; Cassidy, 1984; Butler et al, 1986; Greenswag and Alexander, 1988). This clinical picture, with the addition of delayed motor and language development, was first described in 1956 by Prader, Labhart and Willi and referred to as “Ein Syndrom von Adipositas, Kleinwuchs, Kryptorchidismus und Oligophrenie nach myatonieartigem Zustand im Neugeborenenalter”.

Keywords

Cognitive Profile Nutritional Management Psychological Profile Mild Mental Retardation Social Skill Deficit 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer-Verlag Berlin Heidelberg 1992

Authors and Affiliations

  • L. M. G. Curfs
    • 1
  1. 1.Research DepartmentObservation Center De HondsbergHondsberg 5The Netherlands

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