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Mukoviszidose (zystische Fibrose)

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Pädiatrische Pneumologie

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Zusammenfassung

Die Mukoviszidose oder zystische Fibrose (CF) ist eine erbliche Erkrankung, die sich an exokrinen Drüsen manifestiert und eine abnorme Zusammensetzung des Sekrets zur Folge hat. Von besonderer Bedeutung ist dabei die vermehrte Sekretviskosität, die zu einer Verlegung der sekretabführenden Wege in Drüsen bzw. drüsentragenden Organen führt.

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Authors
  1. U. Stephan
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  2. H. G. Wiesemann
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Editor information

Editors and Affiliations

  1. Klinik für Neonatologie, Medizinische Hochschule Lübeck, Kahlhorststraße 31-35, D-2400, Lübeck, Deutschland

    A. Fenner

  2. Abt. Kinderheilkunde I, Pädiatrische Pneumologie, Medizinische Hochschule Hannover, Kinderklinik, Konstanty-Gutschow-Straße 8, D-3000, Hannover 61, Deutschland

    H. von der Hardt

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© 1985 Springer-Verlag Berlin, Heidelberg

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Stephan, U., Wiesemann, H.G. (1985). Mukoviszidose (zystische Fibrose). In: Fenner, A., von der Hardt, H. (eds) Pädiatrische Pneumologie. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-68541-5_25

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  • DOI: https://doi.org/10.1007/978-3-642-68541-5_25

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-68542-2

  • Online ISBN: 978-3-642-68541-5

  • eBook Packages: Springer Book Archive

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