Congenital Dilatation of the Biliary System

  • Paolo Pavone
  • Roberto Passariello


Congenital dilatation of the biliary ducts is a rare anomaly affecting the extrahepatic or intrahepatic biliary tree, or both. The first description of this pathological entity was that of Vater in 1723 [1], but only in the twentieth century did Vachel and Stevens (1906) and later Caroli (1958) [2] give a more detailed definition, with a classification provided by Todani in 1977 [3].


Bile Duct Biliary Tree Choledochal Cyst Biliary System Biliary Duct 
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Copyright information

© Springer-Verlag Berlin Heidelberg 1997

Authors and Affiliations

  • Paolo Pavone
    • 1
  • Roberto Passariello
    • 1
  1. 1.Istituto di Radiologia, Cattedra IIUniversità degli Studi di Roma “La Sapienza”RomeItaly

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