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Syndromes Associated with Hereditary Deafness

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Pediatric ENT Radiology

Part of the book series: Medical Radiology ((Med Radiol Diagn Imaging))

Abstract

About 1 in 1000 children are affected by severe deafness at birth or during early childhood (i. e. the prelingual period). A further 1 in 1000 children become deaf before adulthood. Most of the studies assessing the genetic causes of deafness address the prelingual forms as these are the most severe, and currently about 60% of these cases are attributed to genetic causes.

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Author information

Authors and Affiliations

  1. Alder Hey Children’s Hospital, Eaton Road, Liverpool, L12 2AP, UK

    A. Fryer MD (Consultant Geneticist)

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  1. A. Fryer MD
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Editors and Affiliations

  1. Bristol Royal Hospital for Sick Children, Paul O’Gorman Building, Upper Maudlin Street, BS2 8BJ, Bristol, UK

    Susan J. King MD

  2. Alder Hey Children’s Hospital, Eaton Road, L12 2AP, Liverpool, UK

    Anne E. Boothroyd MD (Consultant Paediatric Radiologist) (Consultant Paediatric Radiologist)

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© 2003 Springer-Verlag Berlin Heidelberg

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Fryer, A. (2003). Syndromes Associated with Hereditary Deafness. In: King, S.J., Boothroyd, A.E. (eds) Pediatric ENT Radiology. Medical Radiology. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-59367-3_4

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  • DOI: https://doi.org/10.1007/978-3-642-59367-3_4

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-540-00002-0

  • Online ISBN: 978-3-642-59367-3

  • eBook Packages: Springer Book Archive

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