Skip to main content
SpringerLink
Log in
Book cover

Congenital Heart Defects pp 67–71Cite as

Pulmonary atresia with intact ventricular septum

  • Chapter

  • 290 Accesses

Abstract

This is the 13th most common congenital heart disease (1.7% of all congenital heart defects). It occurs in 0.08/1000 live births.

This is a preview of subscription content, log in via an institution.

Chapter
USD   29.95
Price excludes VAT (USA)
  • Available as PDF
  • Read on any device
  • Instant download
  • Own it forever
eBook
USD   84.99
Price excludes VAT (USA)
  • Available as EPUB and PDF
  • Read on any device
  • Instant download
  • Own it forever
Softcover Book
USD   109.99
Price excludes VAT (USA)
  • Compact, lightweight edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info
Hardcover Book
USD   109.99
Price excludes VAT (USA)
  • Durable hardcover edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Purchases are for personal use only

Learn about institutional subscriptions

Preview

Unable to display preview. Download preview PDF.

Unable to display preview. Download preview PDF.

References

  • Albanese SB, Carotti A, Toscano A, Marino B, di Donato RM (2002) Pulmonary atresia with intact ventricular septum and systemic-pulmonary collateral arteries. Ann Thorac Surg 73:1322–1324

    Article  PubMed  Google Scholar 

  • Amodeo A, Keeton BR, Sutherland GR, Monro JL (1991) Pulmonary atresia with intact ventricular septum: is neonatal repair advisable? Eur J Cardiothorac Surg 5:17

    Article  PubMed  CAS  Google Scholar 

  • Billingsley AM, Laks H, Boyce SW, George BL, Santulli T, Williams RG (1989) Definitive repair in patients with pulmonary atresia and intact ventricular septum. J Thorac Cardiovasc Surg 97:746–754

    PubMed  CAS  Google Scholar 

  • Bull C, de Leval MR, Mercanti C, Macartney FJ, Anderson RH (1982) Pulmonary atresia and intact ventricular septum: a revised classification. Circulation 66:266–272

    Article  PubMed  CAS  Google Scholar 

  • Cheung YF, Leung MP, Chau AK (2002) Usefulness of laser-assisted valvotomy with balloon valvoplasty for pulmonary atresia with intact ventricular septum. Am J Cardiol 15:438–442

    Article  Google Scholar 

  • Corno AF, Mazzera E, Marino B, Parisi F, Marcelletti C (1986) Simultaneous patency of ductus arteriosus and surgical shunt in pulmonary atresia with intact ventricular septum. A cause of acute myocardial failure? Scand J Thorac Cardiovasc Surg 20:123–127

    Article  PubMed  CAS  Google Scholar 

  • Corno AF, Giannico S, Marino B, Parisi F, Marcelletti C (1988) Atresia polmonare con setto interventricolare intatto: risultati a distanza. Cardiol 33(Suppl II):18

    Google Scholar 

  • Corno AF, Mazzera E, Marino B, Picardo S, Marcelletti C (1989) Bidirectional cavopulmonary anastomosis. J Am Coll Cardiol 13:74A

    Google Scholar 

  • Corno AF, Giannico S (1993) Echo evaluation of total extracardiac right heart bypass. G Ital Ecogr Cardiovasc 3:1

    Google Scholar 

  • Corno AF, Bertucci C, Ranucci M, Rosti L (1994) Bidirectional superior vena cava to pulmonary artery anastomosis. Int Soc Cardiothorac Surg, 4th World Congr, Abstracts, p 150

    Google Scholar 

  • Corno AF (1996) Considerations on the cavopulmonary connection. Am Coll Cardiol Curr J Rev 5:38

    Google Scholar 

  • Corno AF, Da Cruz E, Lal AB, Milella L, Wilson N (1998) “Controlled reoxygenation” for cyanotic patients. In: Imai Y, Momma K (eds) Proceedings of 2nd World Congress of PCCS. Futura Publishing Co, Armonk, NY, pp 1127–1129

    Google Scholar 

  • Corno AF, Hurni M, Payot M, von Segesser LK (1999) Modified Blalock-Taussig shunt with compensatory properties. Ann Thorac Surg 67:269–270

    Article  PubMed  CAS  Google Scholar 

  • Corno AF, von Segesser LK (1999) Is hypothermia necessary in pediatric cardiac surgery? Eur J Cardiothorac Surg 15:110–111

    Article  PubMed  CAS  Google Scholar 

  • Corno AF (2000) Surgery for congenital heart disease. Curr Opinion Cardiol 15:238–243

    Article  CAS  Google Scholar 

  • Daubeney PE, Delany DJ, Anderson RH, Sandor GG, Slavik Z, Keeton BR, Webber SA (2002) Pulmonary atresia with intact ventricular septum: range of morphology in a population-based study. J Am Coll Cardiol 15:1670–1679

    Article  Google Scholar 

  • De Leval MR, Bull C, Stark J, Anderson RH, Taylor JFN, Macartney FJ (1982) Pulmonary atresia and intact ventricular septum: surgical management based on a revised classification. Circulation 66:272–280

    Article  PubMed  Google Scholar 

  • Freedom RM, Harrington DP (1974) Contributions of intramyocardial sinusoids in pulmonary atresia and intact ventricular septum to a right-sided circular shunt. Br Heart J 36:1061

    Article  PubMed  CAS  Google Scholar 

  • Freedom RM (1983) The morphological variations of pulmonary atresia with intact ventricular septum: guidelines for surgical intervention. Pediatr Cardiol 4:183–188

    Article  PubMed  CAS  Google Scholar 

  • Fyler DC, Buckley LP, Hellenbrand WE, Cohn HE (1980) Report of the New England Regional Infant Care Program. Pediatrics 65(Suppl):375–461

    Google Scholar 

  • Gagliardi MG, Marino B, Papa M, Corno AF, Squitieri C, Marcelletti C (1989) Atresia polmonare a setto integro: indicazioni al trattamento chirurgico neonatale guidato dall`ecocardiografia bidimensionale e Doppler. G Ital Cardiol 19:315–318

    PubMed  CAS  Google Scholar 

  • Giannico S, Corno AF, Nava S, Marino B, Guccione P, Marcelletti C (1989) Inferior vena cava to pulmonary artery extracardiac conduit: echo-Doppler patterns of systemic venous flow. J Am Soc Echocard 2:218

    Google Scholar 

  • Giannico S, Corno AF, Marino B, Cicini MP, Gagliardi MG, Amodeo A, Picardo S, Marcelletti C (1992) Total extracardiac right heart bypass. Circulation 86(Suppl 2):110–117

    Google Scholar 

  • Grabitz RG, Joffres MR, Collins-Nakai RL (1988) Congenital heart disease: incidence in the first year of life. The Alberta heritage pediatric cardiology program. Am J Epidemiol 128:381–388

    PubMed  CAS  Google Scholar 

  • Hoffman JIE, Kaplan S (2002) The incidence of congenital heart disease. J Am Coll Cardiol 39:1890–1900

    Article  PubMed  Google Scholar 

  • Marino B, Corno AF, Pasquini L, Guccione P, Carta MG, Ballerini L, De Simone G, Marcelletti C (1987) Indication for systemic-pulmonary artery shunts guided by two-dimensional and Doppler echocardiography: criteria for patient selection. Ann Thorac Surg 44:495–498

    Article  PubMed  CAS  Google Scholar 

  • Marino B, Giannico S, Pasquini L, Corno AF, Picardo S (1988) Balloon-occlusion of the carotid artery for the angiographic visualization of Blalock-Taussig shunts and pulmonary arteries. Chest 94:267–269

    Article  PubMed  CAS  Google Scholar 

  • Mazzera E, Corno AF, Picardo S, Di Donato RM, Marino B, Costa D, Marcelletti C (1989) Bidirectional cavopulmonary shunts: clinical applications as staged or definitive palliation. Ann Thor-ac Surg 47:415–420

    Article  CAS  Google Scholar 

  • Marcelletti C, Corno AF, Giannico S, Marino B (1990) Inferior vena cava to pulmonary artery extracardiac conduit: a new form of right heart bypass. J Thorac Cardiovasc Surg 100:228–232

    PubMed  CAS  Google Scholar 

  • Minich LL, Tani LY, Ritter S, Williams RV, Shaddy RE, Hawkins JA (2000) Usefulness of the preoperative tricuspid/mitral valve ratio for predicting outcome in pulmonary atresia with intact ventricular septum. Am J Cardiol 85:1325–1328

    Article  PubMed  CAS  Google Scholar 

  • Olley PM, Coceani F, Bodach E (1976) E-type prostaglandins: a new emergency therapy for certain cyanotic congenital heart malformations. Circulations 53:728–731

    Article  CAS  Google Scholar 

  • Powell AJ, Mayer JE, Lang P, Lock JE (2000) Outcome in infants with pulmonary atresia, intact ventricular septum and right ventricle-dependent coronary circulation Am J Cardiol 86:1272–1274

    Article  PubMed  CAS  Google Scholar 

  • Qureshi SA (2001) Collaborative approach in the management of pulmonary atresia with intact ventricular septum. J Intery Cardiol 14:377–384

    Article  CAS  Google Scholar 

  • Sano S, Ishino K, Kawada M, Fujisawa E, Kamada M, Ohtsuki S (2000) Staged biventricular repair of pulmonary atresia or stenosis with intact ventricular septum. Ann Thorac Surg 70:1501–1506

    Article  PubMed  CAS  Google Scholar 

  • Schire V, Sutin GL, Barnard CN (1961) Organic and functional pulmonary atresia with intact ventricular septum. Am J Cardiol 8:100–108

    Article  Google Scholar 

  • Shimpo H, Hayakawa H, Miyake Y, Takabayashi S, Yada I (2000) Strategy for pulmonary atresia and intact ventricular septum. Ann Thorac Surg 70:287–289

    Article  PubMed  CAS  Google Scholar 

  • Takayama H, Sekiguchi A, Chikada M (2001) Pulmonary atresia with intact ventricular septum: long-term results of “one and a half ventricular repair”. Updated in 2001. Ann Thorac Surg 72:2178–2179

    Article  PubMed  CAS  Google Scholar 

  • Tulzer G, Arzt W, Franklin RC, Loughna PV, Mair R, Gardiner HM (2002) Fetal pulmonary valvuloplasty for critical pulmonary stenosis or atresia with intact septum. Lancet 360:1567–1568

    Article  PubMed  Google Scholar 

  • Weber HS (2002) Initial and late results after catheter intervention for neonatal critical pulmonary valve stenosis and atresia with intact ventricular septum: a technique in continual evolution. Catheter Cardiovasc Intery 56:394–399

    Article  Google Scholar 

  • Zuberbuhler JR, Anderson RH (1979) Morphological variations in pulmonary atresia with intact ventricular septum. Br Heart J 41:281

    Article  PubMed  CAS  Google Scholar 

Download references

Author information

Authors and Affiliations

  1. Department of Cardiovascular Surgery, Centre Hospitalier Universitaire Vaudois(CHUV), 46, rue du Bugnon, Lausanne, CH-1011, Switzerland

    Antonio F. Corno MD, FRCS, FETCS

Authors
  1. Antonio F. Corno MD, FRCS, FETCS
    View author publications

    You can also search for this author in PubMed Google Scholar

Rights and permissions

Reprints and permissions

Copyright information

© 2003 Springer-Verlag Berlin Heidelberg

About this chapter

Cite this chapter

Corno, A.F. (2003). Pulmonary atresia with intact ventricular septum. In: Congenital Heart Defects. Steinkopff, Heidelberg. https://doi.org/10.1007/978-3-642-57358-3_10

Download citation

  • DOI: https://doi.org/10.1007/978-3-642-57358-3_10

  • Publisher Name: Steinkopff, Heidelberg

  • Print ISBN: 978-3-642-63245-7

  • Online ISBN: 978-3-642-57358-3

  • eBook Packages: Springer Book Archive

Publish with us

Policies and ethics

Search

Navigation