Zusammenfassung
Das Krankheitsbild der pulmonalen Alveolarproteinosen (PAP) wurde erstmals 1958 detailliert beschrieben. Es handelt sich um eine Gruppe von ungewöhnlichen diffusen Lungenerkrankungen, die durch die Anhäufung großer Mengen phospholipid- und proteinhaltiger Materialien in den Alveolen der Lungen gekennzeichnet ist. Treffend ist daher die Bezeichnung ▸ alveoläre Füllungssyndrome (Abb. 1).
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Griese, M., Tredano, M., Bahuau, M. (2001). Pulmonale Alveolarproteinosen. In: Koletzko, B., Reinhardt, D., Stöckler-Ipsiroglu, S. (eds) Pädiatrie upgrade 2002. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-56123-8_8
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DOI: https://doi.org/10.1007/978-3-642-56123-8_8
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