Abstract
A rare disease, retroperitoneal fibrosis (RF) is characterized by the presence of fibroinflammatory tissue that develops around the abdominal aorta and iliac arteries, often entrapping the ureters. RF has been divided into 2 types: idiopathic RF for which no clear cause is found and secondary RF, whose causes include drugs, radiotherapy, infections, malignant diseases, and trauma [1, 2]. Two patients with anuria caused by bilateral ureteral obstruction due to envelopment and compression of the ureters by an inflammatory retroperitoneal process were reported by Ormond in 1948 [3]. Consequently, idiopathic RF is referred to as Ormond’s disease.
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Acknowledgment
This study was partially supported by the Intractable Disease, supported by the Ministry of Health, Labour, and Welfare of Japan.
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Chiba, K., Kamisawa, T., Tabata, T., Iwasaki, S. (2015). Retroperitoneal Fibrosis. In: Kamisawa, T., Chung, J. (eds) Autoimmune Pancreatitis. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-55086-7_17
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DOI: https://doi.org/10.1007/978-3-642-55086-7_17
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