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Pheochromocytoma

  • Jens ManiEmail author
  • Georg Bartsch
Chapter

Abstract

A pheochromocytoma is a tumor of chromaffin cells, which secrete catecholamines, predominantly norepinephrine, as well as epinephrine, and rarely dopamine. The majority of pheochromocytomas are sporadic, but up to 25 % of cases are hereditary [1]. It may be associated with multiple endocrine neoplasia syndrome, type IIA and type IIB (also known as MEN IIA and MEN IIB), von Hippel-Lindau disease, neurofibromatosis type 1 (von Recklinghausen disease), phakomatosis, and paraganglioma syndromes.

Keywords

Chromaffin Cell Laparoscopic Adrenalectomy Malignant Pheochromocytoma Multiple Endocrine Neoplasia Syndrome Underlying Genetic Mutation 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

References

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    King KS, Pacak K. Familial pheochromocytomas and paragangliomas. Mol Cell Endocrinol. 2014;386:92–100.PubMedCrossRefGoogle Scholar
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    Jimenez C, Rohren E, Habra MA, Rich T, Jimenez P, Ayala-Ramirez M, Baudin E. Current and future treatments for malignant pheochromocytoma and sympathetic paraganglioma. Curr Oncol Rep. 2013;15(4):356–71.PubMedCrossRefGoogle Scholar

Copyright information

© Springer-Verlag Berlin Heidelberg 2014

Authors and Affiliations

  1. 1.Department of UrologyUniversity Hospital FrankfurtFrankfurtGermany

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