• Jens ManiEmail author
  • Georg Bartsch


A pheochromocytoma is a tumor of chromaffin cells, which secrete catecholamines, predominantly norepinephrine, as well as epinephrine, and rarely dopamine. The majority of pheochromocytomas are sporadic, but up to 25 % of cases are hereditary [1]. It may be associated with multiple endocrine neoplasia syndrome, type IIA and type IIB (also known as MEN IIA and MEN IIB), von Hippel-Lindau disease, neurofibromatosis type 1 (von Recklinghausen disease), phakomatosis, and paraganglioma syndromes.


Chromaffin Cell Laparoscopic Adrenalectomy Malignant Pheochromocytoma Multiple Endocrine Neoplasia Syndrome Underlying Genetic Mutation 
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Copyright information

© Springer-Verlag Berlin Heidelberg 2014

Authors and Affiliations

  1. 1.Department of UrologyUniversity Hospital FrankfurtFrankfurtGermany

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