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Other Vascular Tumors

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Abstract

Vascular lesions that arise in infants and children are classified into two groups: neoplasms and malformations. The distinction between the two is the cellular proliferation of vessels that occur in neoplasms, but not in malformations. In this chapter, we will discuss the following neoplasms and focus on their systemic treatment options: kaposiform hemangioendotheliomas and tufted angiomas, including the Kasabach-Merritt phenomenon, hemangiopericytomas, infantile myofibromas, and multifocal lymphangioendotheliomatosis with thrombocytopenia. While generally benign, these are often complicated tumors and as a result of their rarity, they lack the more definitive management approaches of their counterparts, infantile hemangiomas.

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Abbreviations

KHE:

Kaposiform hemangioendothelioma

TA:

tufted angioma

KMP:

Kasabach-Merritt syndrome

IFN:

interferon

HPC:

hemangiopericytoma

MLE-T or MLT:

multifocal lymphangioendotheliomatosis with thrombocytopenia

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Authors and Affiliations

  1. Department of Dermatology, Sharp Rees-Stealy, 7862 El Cajon Blvd, La Mesa, CA, 91941, USA

    Tina S. Chen MD

  2. Department of Pediatrics and Medicine (Dermatology), University of California, San Diego and Rady Children’s Hospital, San Diego, 8010 Frost Street, Suite 602, San Diego, CA, 92123, USA

    Wynnis L. Tom MD

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  1. Tina S. Chen MD
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Correspondence to Wynnis L. Tom MD .

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  1. Pediatric & Adolescent Dermatology, Rady Children's Hospital, San Diego, California, USA

    Wynnis L. Tom

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Chen, T.S., Tom, W.L. (2014). Other Vascular Tumors. In: Tom, W. (eds) Severe Skin Diseases in Children. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-39532-1_10

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