Zusammenfassung
Endokrine Pankreastumoren sind im Vergleich zum Pankreaskarzinom seltene Tumoren. Ihre Häufigkeit nimmt in der westlichen Welt zu, und bedingt durch die günstige Prognose steigt die Zahl der Betroffenen. Die Klinik von Insulinom und Gastrinom kann bereits zielführend sein; in Teilen gilt dies auch für die seltenen Entitäten wie zum Beispiel das VIPom und auch das Glukagonom. Vielfach ist das klinische Bild jedoch nicht zwingend typisch für das Vorliegen eines neuroendokrinen Pankreastumors. Insbesondere die nicht sezernierenden neuroendokrinen Pankreastumoren werden mehrheitlich als Zufallstumor (Inzidentalom) oder erst durch ihren Volumeneffekt klinisch apparent.
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Böhm, B. (2013). Klinische Manifestationen endokriner Tumoren des Pankreas. In: Beger, H., et al. Erkrankungen des Pankreas. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-37964-2_40
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