• Hart IsaacsJr


The histiocytoses are a diverse group of diseases characterized by the infiltration and accumulation of histiocytes primarily within the blood and tissues [1–12]. The term histiocytosis denotes an increase in the number of histiocytes, which consist of two main types of cells: macrophages and dendritic cells [1–3, 6, 8–11]. The histiocytoses range from cytologically benign proliferations of mature cells to clearly malignant ones (Table 8.1).


Hemophagocytic Syndrome Hemophagocytic Lymphohistiocytosis Protein Losing Enteropathy Sinus Histiocytosis Birbeck Granule 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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Copyright information

© Springer-Verlag Berlin Heidelberg 2013

Authors and Affiliations

  • Hart IsaacsJr
    • 1
  1. 1.Department of Pathology Rady Childrens Hospital San DiegoUniversity of California San Diego School of MedicineSan DiegoUSA

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