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Short-, Medium- and Long-Term Outcomes Following Surgery for Disorders of Sex Development (DSD) at Royal Children’s Hospital

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Disorders of Sex Development

Abstract

This chapter summarises the anatomical and psychological outcomes of our own patient cohort at the Royal Children’s Hospital, Melbourne. It describes short-, medium- and long-term results that have been separately published in two articles in the Journal of Pediatric Surgery, one article in the Journal of Urology and one article in the Journal of Pediatric Endocrinology and Metabolism

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References

  • Alizai NK, Thomas DF, Lilford RJ et al (1999) Feminizing genitoplasty for congenital adrenal hyperplasia: what happens at puberty? J Urol 161(5):1588–1591

    Article  PubMed  CAS  Google Scholar 

  • Azziz R, Mulaikal RM, Migeon CJ et al (1986) Congenital adrenal hyperplasia: long-term results following vaginal reconstruction. Fertil Steril 46(6):1011–1014

    PubMed  CAS  Google Scholar 

  • Berenbaum SA, Bailey JM (2003) Effects on gender identity of prenatal androgens and genital appearance: evidence from girls with congenital adrenal hyperplasia. J Clin Endocrinol Metab 88(3):1102–1106

    Article  PubMed  CAS  Google Scholar 

  • Crawford JM, Warne G, Grover S et al (2009) Results from a pediatric surgical centre justify early intervention in disorders of sex development. J Pediatr Surg 44(2):413–416

    Article  PubMed  Google Scholar 

  • Creighton SM, Minto CL, Steele SJ (2001) Objective cosmetic and anatomical outcomes at adolescence of feminising surgery for ambiguous genitalia done in childhood. Lancet 358(9276):124–125

    Article  PubMed  CAS  Google Scholar 

  • Gonzalez R, Fernandes ET (1990) Single-stage feminization genitoplasty. J Urol 143(4):776–778

    PubMed  CAS  Google Scholar 

  • Gupta D, Bhardwaj M, Sharma S et al (2010) Long-term psychological adjustments, satisfaction related to gender and the family equations in disorders of sexual diffrentation with male sex assignment. Pediatr Surg Int 26(10): 958

    PubMed  CAS  Google Scholar 

  • Houk CP, Hughes IA, Ahmed SF et al (2006) Summary of consensus statement on intersex disorders and their management. International Intersex Consensus Conference. Pediatrics 118(2):753–757

    Article  PubMed  Google Scholar 

  • Johnson LL, Bradley SJ, Birkenfeld-Adams AS et al (2004) A parent-report gender identity questionnaire for children. Arch Sex Behav 33(2):105–116

    Article  PubMed  Google Scholar 

  • Vidal I, Gorduzee DB, Haraux E et al (2010) Surgical options in disorders of sex development (dsd) with ambiguous genitalia. Best Pract Res Clin Endocrinol Metab 24(2):311–324

    Google Scholar 

  • Jones BC, O’Brien M, Chase J et al (2009) Early hypospadias surgery may lead to a better long-term psychosexual outcome. J Urol 182(4 Suppl):1744–1749

    Article  PubMed  Google Scholar 

  • Jurgensen M, Hiort O, Holterhus PM et al (2007) Gender role behavior in children with XY karyotype and disorders of sex development. Horm Behav 51(3):443–453

    Article  PubMed  Google Scholar 

  • Lean WL, Deshpande A, Hutson J et al (2005) Cosmetic and anatomic outcomes after feminizing surgery for ambiguous genitalia. J Pediatr Surg 40(12):1856–1860

    Article  PubMed  Google Scholar 

  • Minto CL, Liao LM, Woodhouse CR et al (2003) The effect of clitoral surgery on sexual outcome in individuals who have intersex conditions with ambiguous genitalia: a cross-sectional study. Lancet 361(9365):1252–1257

    Article  PubMed  Google Scholar 

  • Reiner WG, Gearhart JP (2004) Discordant sexual identity in some genetic males with cloacal exstrophy assigned to female sex at birth. N Engl J Med 350(4):333–341

    Article  PubMed  CAS  Google Scholar 

  • Roll MF, Kneppo C, Roth H et al (2006) Feminising genitoplasty: one-stage genital reconstruction in congenital adrenal hyperplasia: 30 years’ experience. Eur J Pediatr Surg 16(5):329–333

    Article  PubMed  CAS  Google Scholar 

  • Schober JM (2001) Sexual behaviors, sexual orientation and gender identity in adult intersexuals: a pilot study. J Urol 165(6 Pt 2):2350–2353

    PubMed  CAS  Google Scholar 

  • Sotiropoulos A, Morishima A, Homsy Y et al (1976) Long-term assessment of genital reconstruction in female pseudohermaphrodites. J Urol 115(5):599–601

    PubMed  CAS  Google Scholar 

  • Varni JW, Seid M, Kurtin PS (2001) PedsQL 4.0: reliability and validity of the Pediatric Quality of Life Inventory version 4.0 generic core scales in healthy and patient populations. Med Care 39(8):800–812

    Article  PubMed  CAS  Google Scholar 

  • Varni JW, Seid M, Knight TS et al (2002) The PedsQL 4.0 Generic Core Scales: sensitivity, responsiveness, and impact on clinical decision-making. J Behav Med 25(2):175–193

    Article  PubMed  Google Scholar 

  • Varni JW, Burwinkle TM, Seid M et al (2003) The PedsQL 4.0 as a pediatric population health measure: feasibility, reliability, and validity. Ambul Pediatr 3(6):329–341

    Article  PubMed  Google Scholar 

  • Warne G, Grover S, Hutson J et al (2005) A long-term outcome study of intersex conditions. J Pediatr Endocrinol Metab 18(6):555–567

    Article  PubMed  Google Scholar 

  • Zucker KJ, Bradley SJ, Oliver G et al (1996) Psychosexual development of women with congenital adrenal hyperplasia. Horm Behav 30(4):300–318

    Article  PubMed  CAS  Google Scholar 

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Correspondence to John M. Hutson .

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© 2012 Springer-Verlag Berlin Heidelberg

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Hutson, J.M., Warne, G.L., Grover, S.R. (2012). Short-, Medium- and Long-Term Outcomes Following Surgery for Disorders of Sex Development (DSD) at Royal Children’s Hospital. In: Hutson, J., Warne, G., Grover, S. (eds) Disorders of Sex Development. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-22964-0_25

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  • DOI: https://doi.org/10.1007/978-3-642-22964-0_25

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  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-22963-3

  • Online ISBN: 978-3-642-22964-0

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