Abstract
Corpus callosum agenesis (CCA) is a relatively frequent malformation. Its exact prevalence in the population is still unknown, as CCA can be completely asymptomatic. This prevalence essentially depends on the population studied and the diagnostic method used and varies between 0.3 % and 0.7 % in the general population (diagnosis by encephalography [1], and hence on selected cases). It reaches 2%–3% for patients showing mental retardation (diagnosis by computed tomography [2]). CCA accounts for 3%– 5 % of all nervous system malformations detected by antenatal ultrasonography (US) and for approximately 50 % of all malformations of the midline [3].
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Garel, C. (2004). Pathology of the Midline. In: MRI of the Fetal Brain. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-18747-6_9
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DOI: https://doi.org/10.1007/978-3-642-18747-6_9
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