Zusammenfassung
Nach der WHO-Einteilung (Richardson et al. 1996) werden Kardiomyopathien als Erkrankungen des Myokards, die mit einer kardialen Dysfunktion einhergehen, definiert. In den letzten Jahren wurde zunehmend deutlich, dass die Ursachen von Kardiomyopathien sehr vielfältig sein können. Es hat sich dabei insbesondere eine erhebliche Bedeutung genetischer Störungen gezeigt. Dementsprechend wurde kürzlich eine neue Definition und Einteilung der Kardiomyopathien von der American Heart Association empfohlen (Maron et al. 2006). Hier werden Kardiomyopathien als eine heterogene Gruppe von Erkrankungen des Myokards definiert, die mit einer mechanischen und/oder elektrischen Dysfunktion assoziiert sind, häufig eine genetische Ursache haben und mit einer Hypertrophie oder Dilatation des Herzens einhergehen können.
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Kilter, H., Böhm, M. (2011). Kardiomyopathien. In: Erdmann, E. (eds) Klinische Kardiologie. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-16481-1_12
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