Chest Surgery pp 237-248 | Cite as

Pulmonary Malformation

  • Stefan Holland-CunzEmail author
Part of the Springer Surgery Atlas Series book series (SPRISURGERY)


From a surgical viewpoint, congenital pulmonary adenomatous malformation (CPAM) and bronchopulmonary sequestration (BPS) are the most relevant inborn pulmonary malformations. However, in rare cases, bronchogenic cysts and congenital lobar emphysema also need surgical intervention. CPAM (Fig. 22.1) is considered to represent a hamartomatous change in the tertiary bronchioles, with an incidence of 1 in 25,000–35,000 live births. BPS has an estimated incidence of 0.15–1.7 % in the general population and is defined as a region of lung parenchyma that lacks a normal connection to the tracheobronchial tree and possesses an anomalous systemic blood supply (Fig. 22.2). There is a high proportion of mixed-type lesions, suggesting that CPAM and BPS may have the same developmental ancestry.


Esophageal Atresia Bronchogenic Cyst Pulmonary Sequestration Congenital Lobar Emphysema Anterior Serratus 
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Copyright information

© Springer-Verlag Berlin Heidelberg 2015

Authors and Affiliations

  1. 1.Department of Pediatric SurgeryUniversity Children’s HospitalBaselSwitzerland

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