Advertisement

Chest Surgery pp 237-248 | Cite as

Pulmonary Malformation

  • Stefan Holland-CunzEmail author
Chapter
Part of the Springer Surgery Atlas Series book series (SPRISURGERY)

Abstract

From a surgical viewpoint, congenital pulmonary adenomatous malformation (CPAM) and bronchopulmonary sequestration (BPS) are the most relevant inborn pulmonary malformations. However, in rare cases, bronchogenic cysts and congenital lobar emphysema also need surgical intervention. CPAM (Fig. 22.1) is considered to represent a hamartomatous change in the tertiary bronchioles, with an incidence of 1 in 25,000–35,000 live births. BPS has an estimated incidence of 0.15–1.7 % in the general population and is defined as a region of lung parenchyma that lacks a normal connection to the tracheobronchial tree and possesses an anomalous systemic blood supply (Fig. 22.2). There is a high proportion of mixed-type lesions, suggesting that CPAM and BPS may have the same developmental ancestry.

Keywords

Esophageal Atresia Bronchogenic Cyst Pulmonary Sequestration Congenital Lobar Emphysema Anterior Serratus 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

Selected Bibliography

  1. Ch’in KY, Tang MY (1949) Congenital adenomatoid malformation of one lobe of a lung with general anasarca. Arch Pathol 48:221–229Google Scholar
  2. Davenport M, Warne SA, Cacciaguerra S, Patel S, Greenough A, Nicolaides K (2004) Current outcome of antenally diagnosed cystic lung disease. J Pediatr Surg 39:549–556PubMedCrossRefGoogle Scholar
  3. Pryce DM (1946) Lower accessory pulmonary artery with intralobar sequestration of the lung. A report of seven cases. J Pathol Bacteriol 58:457PubMedCrossRefGoogle Scholar
  4. Rokitansky C (1861) Lehrbuch der pathologischen anatomie, 3rd edn. Braumüller, ViennaGoogle Scholar
  5. Stanton M, Njere I, Ade-Ajayi N, Patel S, Davenport M (2009) Systematic review and meta-analysis of the congenital cystic lung lesions. J Pediatr Surg 44:1027–1033PubMedCrossRefGoogle Scholar
  6. Stocker JT, Madewell JE, Drake RM (1977) Congenital cystic adenomatoid malformation of the lung. Classification and morphological spectrum. Hum Pathol 8:155–171PubMedCrossRefGoogle Scholar

Copyright information

© Springer-Verlag Berlin Heidelberg 2015

Authors and Affiliations

  1. 1.Department of Pediatric SurgeryUniversity Children’s HospitalBaselSwitzerland

Personalised recommendations