Abstract
From a surgical viewpoint, congenital pulmonary adenomatous malformation (CPAM) and bronchopulmonary sequestration (BPS) are the most relevant inborn pulmonary malformations. However, in rare cases, bronchogenic cysts and congenital lobar emphysema also need surgical intervention. CPAM (Fig. 22.1) is considered to represent a hamartomatous change in the tertiary bronchioles, with an incidence of 1 in 25,000–35,000 live births. BPS has an estimated incidence of 0.15–1.7 % in the general population and is defined as a region of lung parenchyma that lacks a normal connection to the tracheobronchial tree and possesses an anomalous systemic blood supply (Fig. 22.2). There is a high proportion of mixed-type lesions, suggesting that CPAM and BPS may have the same developmental ancestry.
Access this chapter
Tax calculation will be finalised at checkout
Purchases are for personal use only
Selected Bibliography
Ch’in KY, Tang MY (1949) Congenital adenomatoid malformation of one lobe of a lung with general anasarca. Arch Pathol 48:221–229
Davenport M, Warne SA, Cacciaguerra S, Patel S, Greenough A, Nicolaides K (2004) Current outcome of antenally diagnosed cystic lung disease. J Pediatr Surg 39:549–556
Pryce DM (1946) Lower accessory pulmonary artery with intralobar sequestration of the lung. A report of seven cases. J Pathol Bacteriol 58:457
Rokitansky C (1861) Lehrbuch der pathologischen anatomie, 3rd edn. Braumüller, Vienna
Stanton M, Njere I, Ade-Ajayi N, Patel S, Davenport M (2009) Systematic review and meta-analysis of the congenital cystic lung lesions. J Pediatr Surg 44:1027–1033
Stocker JT, Madewell JE, Drake RM (1977) Congenital cystic adenomatoid malformation of the lung. Classification and morphological spectrum. Hum Pathol 8:155–171
Author information
Authors and Affiliations
Corresponding author
Editor information
Editors and Affiliations
Rights and permissions
Copyright information
© 2015 Springer-Verlag Berlin Heidelberg
About this chapter
Cite this chapter
Holland-Cunz, S. (2015). Pulmonary Malformation. In: Dienemann, H., Hoffmann, H., Detterbeck, F. (eds) Chest Surgery. Springer Surgery Atlas Series. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-12044-2_22
Download citation
DOI: https://doi.org/10.1007/978-3-642-12044-2_22
Published:
Publisher Name: Springer, Berlin, Heidelberg
Print ISBN: 978-3-642-12043-5
Online ISBN: 978-3-642-12044-2
eBook Packages: MedicineMedicine (R0)