Diagnosis and Treatment of Soft Tissue Sarcomas

  • Miklós Szendrői
  • Zoltan Sápi
  • Kinga Karlinger
  • Zsuzsa Pápai
Chapter
Part of the European Instructional Lectures book series (EICL, volume 10)

Abstract

Soft tissue tumours form a very heterogeneous group containing more than 200 clinico-pathological sub-types [15]. According to the WHO classification, all tumours originating from non-epithelial tissues, all extra-skeletal bone and cartilage-forming tumours, tumours of the peripheral nerves and neuro-ectodermal tissues are discussed here except those that develop from the reticuloendothelial system, the glia and parenchymal connective tissue. Whilst the benign soft tissue tumours are relatively common, the soft tissue sarcomas (STS) are rare, their distribution being 100:1. The annual incidence of STS is around 30/1 million inhabitants. They comprise less than 1% of all malignant tumours in adults but 15% of all paediatric malignancies [32]. The consequence of this is that the general pathologist and orthopaedic surgeon may not meet these types of tumours for years. The rarity of the STS underlines that these patients should be sent to tumour centres where enough experience is accumulated and specialized pathologists, surgeons, oncologists and radiotherapists give interdisciplinary treatment according to multi-modal protocols.

Keywords

Soft Tissue Sarcoma Synovial Sarcoma Malignant Peripheral Nerve Sheath Tumour Soft Tissue Sarcoma Desmoplastic Small Round Cell Tumour 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© EFORT 2010

Authors and Affiliations

  • Miklós Szendrői
    • 1
  • Zoltan Sápi
  • Kinga Karlinger
  • Zsuzsa Pápai
  1. 1.Semmelweis University BudapestBudapestHungary

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