Myocardial Diseases (Cardiomyopathies)
Cardiomyopathies are a group of diseases with different etiologies, all characterized by cardiac muscles dysfunction. Cardiomyopathies are an important cause of arrhythmias and sudden cardiac death in young patients. Three types of cardiomyopathies have been described by the World Health Organization (WHO):
Hypertrophic cardiomyopathy (HCM) is characterized by inappropriate left ventricular hypertrophy, with preservation of the myocardium contractility.
Dilated cardiomyopathy (DCM) is characterized by ventricular dilatation with contractility dysfunction. Most secondary causes of cardiomyopathies are related to this type.
Restrictive cardiomyopathy (RCM) is characterized by diastolic dysfunction and restricted contractility.
Other uncommon forms of cardiomyopathies include: athlete's heart, arrhythmogenic right ventricular dysplasia (ARVD), noncompaction cardiomyopathy (NCCM), and peripartum cardiomyopathy. Each of the classic three forms and the uncommon forms of cardiomyopathies are discussed below.
KeywordsGlycogen Storage Disease Constrictive Pericarditis Restrictive Cardiomyopathy Arrhythmogenic Right Ventricular Dysplasia Peripartum Cardiomyopathy
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.
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