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Enhanced S-Cone Syndrome

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Inherited Chorioretinal Dystrophies
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Abstract

Enhanced S-cone syndrome (ESCS) is a rare autosomally recessively inherited disorder usually characterised by nummular pigmentary deposition in the region of the vascular arcades at the level of the RPE. The disorder was first so described in 1990.

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Correspondence to Graham E. Holder .

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Holder, G.E. (2014). Enhanced S-Cone Syndrome. In: Puech, B., De Laey, JJ., Holder, G. (eds) Inherited Chorioretinal Dystrophies. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-69466-3_14

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  • DOI: https://doi.org/10.1007/978-3-540-69466-3_14

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  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-540-69464-9

  • Online ISBN: 978-3-540-69466-3

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