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Adolescents with Chronic Kidney Disease pp 81–92Cite as

Congenital Anomalies of the Kidney and Urinary Tract in Adolescents

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Abstract

Congenital anomalies of the kidney and urinary tract are a heterogeneous group of disorders which represent the most common cause of chronic kidney disease in children and adolescents. Children are most often diagnosed in the antenatal and neonatal period given the widespread use of antenatal ultrasound; however, late diagnoses do occur and clinicians should recognize potential presenting signs and symptoms. Care of children with chronic kidney disease due to congenital anomalies of the kidney and urinary tract should be undertaken by a multidisciplinary team that includes both a pediatric urologist and pediatric nephrologist. Treatment involves surgical interventions and management of bladder dysfunction in some cases, as well as medical management of the complications of chronic kidney disease. Particular attention should be paid to the adolescent with chronic kidney disease due to congenital anomalies of the kidney and urinary tract as puberty is a time of more rapid kidney disease progression. For those children who do progress to end-stage renal disease, outcomes with renal transplantation are superior in this group of patients as compared to other causes of renal disease.

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Author information

Authors and Affiliations

  1. Department of Pediatrics, Division of Nephrology, University of California San Francisco, San Francisco, CA, USA

    Erica Winnicki

  2. Department of Urology, University of California San Francisco, San Francisco, CA, USA

    Hillary Copp

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  1. Erica Winnicki
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  2. Hillary Copp
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Correspondence to Erica Winnicki .

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Editors and Affiliations

  1. Department of Pediatric Nephrology, UC Davis Medical Center, Sacramento, CA, USA

    Maha N. Haddad

  2. Department of Pediatrics, Division of Nephrology, University of California San Francisco, San Francisco, CA, USA

    Erica Winnicki

  3. Department of Pediatrics, UC Davis Children’s Hospital, Sacramento, CA, USA

    Stephanie Nguyen

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Winnicki, E., Copp, H. (2019). Congenital Anomalies of the Kidney and Urinary Tract in Adolescents. In: Haddad, M., Winnicki, E., Nguyen, S. (eds) Adolescents with Chronic Kidney Disease. Springer, Cham. https://doi.org/10.1007/978-3-319-97220-6_5

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  • DOI: https://doi.org/10.1007/978-3-319-97220-6_5

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  • Online ISBN: 978-3-319-97220-6

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