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Auto-Inflammatory Syndromes pp 277–286Cite as

Idiopathic Recurrent Acute Pericarditis

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Abstract

Recurrent pericarditis is idiopathic in majority of patients and is frequently precipitated by a well-defined trigger such as injury or infection. Rigorous invasive diagnostic workup is not indicated unless risk factors for secondary causes are present. Idiopathic recurrent acute pericarditis (IRAP) can rarely be complicated by myocarditis, constrictive pericarditis, and pericardial tamponade. IRAP’s pathophysiology shares features with the autoinflammatory syndromes; hence, colchicine and anakinra, an interleukin 1 receptor antagonist, have proven effective therapeutic strategies in patients refractory or intolerant to nonsteroid anti-inflammatory medications and steroids.

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Authors and Affiliations

  1. Division of Rheumatology, Allergy and Immunology, Stony Brook University, Stony Brook, NY, USA

    Apostolos Kontzias

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  1. Apostolos Kontzias
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Correspondence to Apostolos Kontzias .

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  1. New York University School of Medicine, New York, NY, USA

    Petros Efthimiou

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Kontzias, A. (2019). Idiopathic Recurrent Acute Pericarditis. In: Efthimiou, P. (eds) Auto-Inflammatory Syndromes. Springer, Cham. https://doi.org/10.1007/978-3-319-96929-9_20

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  • DOI: https://doi.org/10.1007/978-3-319-96929-9_20

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-96928-2

  • Online ISBN: 978-3-319-96929-9

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