Part of the Advances in Experimental Medicine and Biology book series (AEMB, volume 1085)
Extracellular Matrix: Alport Syndrome
Patients present with X-linked inheritance; Alport syndrome occurs in approximately 1 in 50,000 newborns.
The systemic features include progressive interstitial nephritis, renal failure by the fifth decade, and neurosensory deafness.
KeywordsExtracellular matrix Alport syndrome
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