Abstract
Primary tumors of the lung and heart are very rare in children as compared to metastatic disease which, although uncommon, is still seen more often. Thus, three entities are discussed here, pleuropulmonary blastoma, inflammatory myofibroblastic tumor, and histiocytoid cardiomyopathy, in each of which there has been recent progress in understanding their molecular pathogenesis. Discussion will also focus on the pathologic and molecular features of cardiac fibroma and NUT midline carcinoma.
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Shehata, B.M., Khoshnam, N., Husain, A.N. (2018). Cardiovascular and Respiratory Systems. In: Furtado, L., Husain, A. (eds) Precision Molecular Pathology of Neoplastic Pediatric Diseases . Molecular Pathology Library. Springer, Cham. https://doi.org/10.1007/978-3-319-89626-7_12
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DOI: https://doi.org/10.1007/978-3-319-89626-7_12
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