Darier’s Disease

  • Enzo Errichetti
  • Giuseppe Stinco


Darier’s disease is an uncommon, autosomal-dominant inherited disorder. It is characterized by greasy, hyperkeratotic, skin-colored, or yellowish-brown papules that show a characteristic dermatoscopic pattern which consists of a central yellowish-brownish area of different morphologies (“star-like,” branched, polygonal, or roundish-oval), generally surrounded by a whitish halo. Sometimes it is possible to appreciate dotted, linear, and/or irregular vessels, mainly located at the periphery of the lesions.


Darier’s disease Inherited disorders Hyperkeratotic papules Star-like aspect Irregular vessels 


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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  1. 1.Department of Medical Area, Institute of DermatologyUniversity of UdineUdineItaly

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