Abstract
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Double-chambered right ventricle (DCRV) occurs in approximately 1% of patients with congenital heart disease. The right ventricle (RV) is divided by anomalous muscle bundles into a higher-pressure proximal chamber and lower-pressure distal chamber. The physiology is defined by right ventricular pressure overload of the RV inflow chamber. Depending on the degree of obstruction, the clinical course varies significantly in severity and clinical presentation.
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Abbreviations
- ACC:
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American College of Cardiology
- AHA:
-
American Heart Association
- ASD:
-
Atrial septal defect
- DCRV:
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Double-chamber right ventricle
- MRI:
-
Magnetic resonance imaging
- RV:
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Right ventricle
- RVSP:
-
Right ventricular systolic pressure
- TEE:
-
Transesophageal echocardiography
- TR:
-
Tricuspid regurgitation
- TTE:
-
Transthoracic echocardiography
- VSD:
-
Ventricular septal defect
- WHO:
-
World Health Organization
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Valle, C. (2018). Double-Chambered Right Ventricle (DCRV). In: DeFaria Yeh, D., Bhatt, A. (eds) Adult Congenital Heart Disease in Clinical Practice. In Clinical Practice. Springer, Cham. https://doi.org/10.1007/978-3-319-67420-9_21
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DOI: https://doi.org/10.1007/978-3-319-67420-9_21
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