Congenital Hernia of Umbilical Cord (CHUC)
During early fetal life, there is physiological herniation of a greater portion of the intestines into the proximal part of the umbilical cord, which is called extracelomic cavity. At about 10–12 weeks gestation, intestines withdraw into the abdominal cavity after completion of the bowel rotation, the umbilical ring mostly closes, and the extracelomic cavity disappears leaving behind Wharton’s jelly and umbilical vessels in the cord.
In rare instances, the umbilical ring does not close, and variable portions of the intestines remain in the extracelomic cavity to present at birth as congenital hernia into the umbilical cord, which is a normal developmental herniation in early fatal life but it may persist and to be manifested at birth as a 18 cystic swelling at the fetal end of the cord. The wall of the hernia formed of amnion and peritoneum; consequently, the intestinal loops within the sac are readily visible.
KeywordsCongenital umbilical hernia Extracelomic Cord cyst Umbilicus Cutis
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