Gedye Dementia Scale for Down Syndrome

  • Emoke Jozsvai
  • Spencer Hewitt
  • Angela Gedye


The term “dementia” refers to deterioration in intellectual functioning or the development of multiple cognitive deficits affecting memory, language, comprehension, and activities of daily living. There are many types of dementia that occur in the general population and in those with intellectual disability (ID). Dementia in Alzheimer Disease (DAD) is the most common form of dementia in Down syndrome (DS). Its clinical manifestation increases with aging from 8%, in those between 35 and 40 years old, to approximately 22%, for those aged 40+. For individuals in the 60+ age group, the rate is estimated to be 69% [1–4]. Among institutionalized individuals with DS the rate of dementia has been reported to be as high as 77% [5]. However, other types of progressive dementia (e.g., vascular dementia), reversible dementias (e.g., untreated hypothyroidism), and conditions that mimic dementia also occur in adults with ID [6]. The pattern and symptoms of DAD in adults with DS are similar to those observed in the general population [7, 8], except that the decline in DS adults starts from a significantly lower level of functioning and from a younger age [9].


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Copyright information

© Springer International Publishing AG 2018

Authors and Affiliations

  • Emoke Jozsvai
    • 1
  • Spencer Hewitt
    • 2
  • Angela Gedye
    • 3
  1. 1.Department of PsychologySurrey Place CentreTorontoCanada
  2. 2.Ryerson UniversityTorontoCanada
  3. 3.Private Practice PsychologistVancouverCanada

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