Epileptic encephalopathies are severe diseases of the brain starting at an early age of childhood and more usually in infancy. They manifest with (1) frequent and various types of epileptic seizures which are resistant to treatment and (2) cognitive, behavioural and neurological deficits which often worsen with time (progressive). West, Lennox-Gastaut and Dravet syndrome are described in this chapter. In addition to addressing seizures, holistic care for patients with epileptic encephalopathies must involve a multidisciplinary team that includes specialists in psychotherapy, physical, occupational and speech therapy and social work. Families need significant and continuous multiple support.
KeywordsWest syndrome Lennox-Gastaut syndrome Dravet syndrome Cognitive decline Psychological support Treatment SUDEP