Epileptic Encephalopathies

  • Thalia Valeta


Epileptic encephalopathies are severe diseases of the brain starting at an early age of childhood and more usually in infancy. They manifest with (1) frequent and various types of epileptic seizures which are resistant to treatment and (2) cognitive, behavioural and neurological deficits which often worsen with time (progressive). West, Lennox-Gastaut and Dravet syndrome are described in this chapter. In addition to addressing seizures, holistic care for patients with epileptic encephalopathies must involve a multidisciplinary team that includes specialists in psychotherapy, physical, occupational and speech therapy and social work. Families need significant and continuous multiple support.


West syndrome Lennox-Gastaut syndrome Dravet syndrome Cognitive decline Psychological support Treatment SUDEP 


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Copyright information

© Springer International Publishing AG 2017

Authors and Affiliations

  • Thalia Valeta
    • 1
    • 2
  1. 1.First Neurology and Psychiatry ClinicUniversity of Athens, Aeginition HospitalAthensGreece
  2. 2.Department of Clinical Neurophysiology and EpilepsiesSt. Thomas’ HospitalLondonUK

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