Abstract
Primary pediatric cardiac tumors are rare, with a reported incidence of less than 0.1%. Historically, cardiac tumors have been defined by histological features. More recently, noninvasive imaging, particularly cardiac magnetic resonance (CMR), has become the primary diagnostic modality for anatomic and tissue characterization. The majority of pediatric cardiac tumors are benign and do not need surgical intervention. However, even histologically, benign tumors can become problematic due to their size and location. Benign cardiac tumors causing inflow or outflow obstruction or compression of cardiac structures often require surgical removal. Additionally, benign cardiac tumors can lead to arrhythmias requiring ablation. Using image guidance for transcatheter or even open-ablation techniques may lead to improved results. While malignant primary cardiac tumors are rarer than their benign counterparts, they should always be considered for surgical removal given the 1-year survival rate of ~10% without resection. Cardiac tumors are often complex 3-dimensional (3D) structures within or around the heart. Using 3D printing in procedural planning can be a valuable tool to improve targeted approaches and ultimately outcomes.
Keywords
This is a preview of subscription content, log in via an institution.
Buying options
Tax calculation will be finalised at checkout
Purchases are for personal use only
Learn about institutional subscriptionsReferences
Leja MJ, Shah DJ, Reardon MJ. Primary cardiac tumors. Tex Heart Inst J. 2011;38:261–2.
Gunther T, Schreiber C, Noebauer C, Eicken A, Lange R. Treatment strategies for pediatric patients with primary cardiac and pericardial tumors: a 30-year review. Pediatr Cardiol. 2008;29:1071–6.
Padalino MA, Reffo E, Cerutti A, Favero V, Biffanti R, Vida V, Stellin G, Milanesi O. Medical and surgical management of primary cardiac tumours in infants and children. Cardiol Young. 2014;24:268–74.
Freedom RM, Lee KJ, MacDonald C, Taylor G. Selected aspects of cardiac tumors in infancy and childhood. Pediatr Cardiol. 2000;21:299–316.
Uzun O, Wilson DG, Vujanic GM, Parsons JM, De Giovanni JV. Cardiac tumours in children. Orphanet J Rare Dis. 2007;2:11.
Cho JM, Danielson GK, Puga FJ, Dearani JA, McGregor CG, Tazelaar HD, Hagler DJ. Surgical resection of ventricular cardiac fibromas: early and late results. Ann Thorac Surg. 2003;76:1929–34.
Beroukhim RS, Prakash A, Buechel ER, Cava JR, Dorfman AL, Festa P, Hlavacek AM, Johnson TR, Keller MS, Krishnamurthy R, Misra N, Moniotte S, Parks WJ, Powell AJ, Soriano BD, Srichai MB, Yoo SJ, Zhou J, Geva T. Characterization of cardiac tumors in children by cardiovascular magnetic resonance imaging: a multicenter experience. J Am Coll Cardiol. 2011;58:1044–54.
Author information
Authors and Affiliations
Corresponding author
Editor information
Editors and Affiliations
Rights and permissions
Copyright information
© 2017 Springer International Publishing AG
About this chapter
Cite this chapter
Moore, R.A., Taylor, M.D. (2017). Cardiac Tumors. In: Farooqi, K. (eds) Rapid Prototyping in Cardiac Disease. Springer, Cham. https://doi.org/10.1007/978-3-319-53523-4_15
Download citation
DOI: https://doi.org/10.1007/978-3-319-53523-4_15
Published:
Publisher Name: Springer, Cham
Print ISBN: 978-3-319-53522-7
Online ISBN: 978-3-319-53523-4
eBook Packages: MedicineMedicine (R0)