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Congenital Mitral Valve Anomalies

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Congenital Heart Disease in Pediatric and Adult Patients

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Abstract

Congenital anomalies of the mitral valve represent a broad spectrum of lesions that are often associated with other congenital heart anomalies. The reported incidence of congenital anomalies of the mitral valve in an echocardiographic study of 13,400 subjects was 0.5 % (Banerjee et al. 1995). These lesions affect valve function in a variable manner. When indicated, surgical intervention results in good long-term results (Hoashi et al. 2010; Lee et al. 2010; Serraf et al. 2000). In the last few years, enhanced knowledge of the functional as well as anatomical aspects of these lesions accompanied by concomitant significant advances in the diagnosis as well as anesthetic and surgical management has contributed to improved outcomes. This chapter provides an overview of the different congenital malformations that can affect the mitral valve excluding mitral valve anomalies in atrioventricular septal defects (AVSD) and univentricular hearts and focuses on the anesthetic and surgical management of these congenital mitral anomalies.

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Authors and Affiliations

  1. Harefield Hospital, London, UK

    Shahzad G. Raja BSc,MBBS(Hons.),MRCS,FRCS(C-Th)

  2. Royal Brompton and Harefield NHS Foundation Trust, London, UK

    I. Gavin Wright MB ChB, FCA (SA)

Authors
  1. Shahzad G. Raja BSc,MBBS(Hons.),MRCS,FRCS(C-Th)
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  2. I. Gavin Wright MB ChB, FCA (SA)
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Correspondence to Shahzad G. Raja BSc,MBBS(Hons.),MRCS,FRCS(C-Th) .

Editor information

Editors and Affiliations

  1. Cardiac Anesthesiology Department, Anesthesiology Research Center Shahid Beheshti University of Medical Sciences, Tehran, Iran

    Ali Dabbagh

  2. Kaiser Permanente Los Angeles Medical Center Division of Cardiac Anesthesiology, Los Angeles, California, USA

    Antonio Hernandez Conte

  3. Department of Anesthesiology, Cedars-Sinai Medical Center, Los Angeles, California, USA

    Lorraine Lubin

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Raja, S.G., Wright, I.G. (2017). Congenital Mitral Valve Anomalies. In: Dabbagh, A., Conte, A., Lubin, L. (eds) Congenital Heart Disease in Pediatric and Adult Patients. Springer, Cham. https://doi.org/10.1007/978-3-319-44691-2_22

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  • DOI: https://doi.org/10.1007/978-3-319-44691-2_22

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