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Sickle Cell Disease

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Part of the book series: Respiratory Medicine ((RM))

Abstract

Sickle cell disease is an illness that predominantly affects African Americans in the United States, where it is an important and under-recognized problem. In this country, research funding for sickle cell disease is substantially lower than that for other monogenic diseases such as cystic fibrosis. Such disparities in research funding lead to limited knowledge translation or therapeutic innovation, ultimately affecting the care of patients with sickle cell disease. Moreover, disparities in access to and quality of healthcare affect outcomes in sickle cell disease, including those for respiratory health. Several steps, including increased research funding from private foundations and government agencies, standardization and accreditation for the delivery of care, and other measures to reduce healthcare disparities (e.g., improved management of pain and co-existing asthma), should have substantial benefits for subjects with SCD, including prolonging and improving life while reducing healthcare costs.

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Correspondence to Michael R. DeBaun MD, MPH .

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Glassberg, J., DeBaun, M.R. (2017). Sickle Cell Disease. In: Celedón, J. (eds) Achieving Respiratory Health Equality. Respiratory Medicine. Humana Press, Cham. https://doi.org/10.1007/978-3-319-43447-6_11

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  • DOI: https://doi.org/10.1007/978-3-319-43447-6_11

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  • Publisher Name: Humana Press, Cham

  • Print ISBN: 978-3-319-43445-2

  • Online ISBN: 978-3-319-43447-6

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