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Hemangiopericytoma

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Adult CNS Radiation Oncology

Abstract

Hemangiopericytoma (HPC) is a rare type of mesenchymal tumor associated with an aggressive phenotype with a predilection toward poor local control and subsequent metastasis. As these tumors cannot be readily distinguished from other tumorigenic entities by radiographic imaging alone, a tissue is required to make an effective diagnosis. The ability to make this diagnosis is vital in the context of HPC as this tumor type requires an aggressive therapeutic approach and vigilant follow-up. The current therapeutic strategy for HPC involves maximal safe surgical resection followed by adjuvant radiotherapy. Repeat resection or salvage radiotherapy is also indicated at the time of recurrence or development of metastasis. By maintaining an attentive follow-up schedule for patients with HPC, clinicians may be able to improve patient outcomes.

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Author information

Authors and Affiliations

  1. Department of Pathology, MD Anderson Cancer Center, Houston, TX, USA

    Vincent Bernard

  2. Department of Radiation Oncology, MD Anderson Cancer Center, Houston, TX, USA

    Amol J. Ghia

Authors
  1. Vincent Bernard
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  2. Amol J. Ghia
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Corresponding author

Correspondence to Amol J. Ghia .

Editor information

Editors and Affiliations

  1. Department of Radiation Oncology, Keck School of Medicine of USC, Norris Cancer Hospital, Los Angeles, California, USA

    Eric L. Chang

  2. Department of Radiation Oncology, Mayo Clinic, Rochester, Minnesota, USA

    Paul D. Brown

  3. Department of Radiation Oncology, University of Washington Medical Center, Seattle, Washington, USA

    Simon S. Lo

  4. Department of Radiation Oncology, Sunnybrook Health Sciences Centre, University of Toronto, Toronto, Ontario, Canada

    Arjun Sahgal

  5. Department of Radiation Oncology, Taussig Cancer Institute Cleveland Clinic, Cleveland, Ohio, USA

    John H. Suh

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Bernard, V., Ghia, A.J. (2018). Hemangiopericytoma. In: Chang, E., Brown, P., Lo, S., Sahgal, A., Suh, J. (eds) Adult CNS Radiation Oncology. Springer, Cham. https://doi.org/10.1007/978-3-319-42878-9_21

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  • DOI: https://doi.org/10.1007/978-3-319-42878-9_21

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-42877-2

  • Online ISBN: 978-3-319-42878-9

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