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Choroid Plexus Tumors

  • Christina Snider
  • John H. Suh
  • Erin S. MurphyEmail author
Chapter

Abstract

Choroid plexus tumors (CPT) are rare tumors of the neuroepithelial tissue of the brain that are most common in young children. In adults, they arise most frequently in the fourth ventricle, often presenting with hydrocephalus due to overproduction of CSF. There are three histopathological classifications of choroid plexus tumors: choroid plexus papilloma (CPP), atypical choroid plexus papilloma (ACP), and choroid plexus carcinoma (CPC). Histology and extent of surgical resection are prognostic for choroid plexus tumors. Curative treatment for CPP and ACP is typically maximum surgical resection, although recurrence rates are higher in cases of ACP. CPP and ACP have better prognosis than CPC, which often requires multiple modalities for treatment.

Keywords

Choroid plexus Choroid plexus papilloma Atypical choroid plexus papilloma Choroid plexus carcinoma Radiation therapy Stereotactic radiosurgery 

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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  • Christina Snider
    • 1
  • John H. Suh
    • 2
    • 3
  • Erin S. Murphy
    • 2
    • 3
    Email author
  1. 1.Cleveland Clinic Lerner College of MedicineClevelandUSA
  2. 2.Department of Radiation OncologyTaussig Cancer Institute, Cleveland ClinicClevelandUSA
  3. 3.Rose Ella Burkhardt Brain Tumor and Neuro-oncology CenterCleveland ClinicClevelandUSA

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