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Scleroderma pp 533–550Cite as

Overlooked Manifestations

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Abstract

Systemic sclerosis (SSc) is a heterogeneous disease with well-described traditional clinical manifestations, such as Raynaud’s phenomenon, dermal sclerosis, esophageal dysmotility, calcinosis, and telangiectasia. Because the clinical presentation can be complex and involve multiple organ systems, there are several other manifestations that often go unrecognized but cause significant morbidity. This chapter discusses a few such manifestations, including neurological manifestations, audiovestibular disease, oral complications, thyroid dysfunction, liver disease, avascular necrosis of bone, bladder dysfunction, and erectile dysfunction.

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Authors and Affiliations

  1. Division of Rheumatology, Rhode Island Hospital, Providence, RI, USA

    Edward V. Lally MD

  2. Department of Medicine/Rheumatology, Johns Hopkins Scleroderma Center, Baltimore, MD, USA

    Ami A. Shah MD, MHS

  3. Department of Medicine/Rheumatology, The Johns Hopkins University School of Medicine, Baltimore, MD, USA

    Fredrick M. Wigley MD

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  1. Edward V. Lally MD
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  2. Ami A. Shah MD, MHS
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  3. Fredrick M. Wigley MD
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Correspondence to Edward V. Lally MD .

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Editors and Affiliations

  1. Feinberg School of Medicine, Northwestern University, Chicago, Illinois, USA

    John Varga

  2. Division of Medicine, Department of Inflammation, Centre for Rheumatology and Connective Tissue Diseases, UCL Division of Medicine, Royal Free Hospital, London, United Kingdom

    Christopher P. Denton

  3. Division of Rheumatology, Johns Hopkins University, Baltimore, Maryland, USA

    Fredrick M. Wigley

  4. Service de Rhumatologie A, INSERMU1016, Universit. Paris Descartes, Hôpital Cochin, Paris, France

    Yannick Allanore

  5. Department of Allergy and Rheumatology, Nippon Medical School, Graduate School of Medicine, Tokyo, Japan

    Masataka Kuwana

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Lally, E.V., Shah, A.A., Wigley, F.M. (2017). Overlooked Manifestations. In: Varga, J., Denton, C., Wigley, F., Allanore, Y., Kuwana, M. (eds) Scleroderma. Springer, Cham. https://doi.org/10.1007/978-3-319-31407-5_38

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