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Extramammary Paget’s Disease

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Rare Genitourinary Tumors

Abstract

Extramammary Paget’s disease (EMPD) is a rare intraepithelial malignancy that has only been a few hundred times in the literature with level 4 evidence. The precise incidence is unknown. However, little is known regarding optimal treatment and prognostic factors. Due to poor understanding of the condition, it can remain undiagnosed for a number of years prior to treatment, and with individual patient numbers remaining small across centers, it becomes difficult to build up a true understanding of the disease process.

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Authors and Affiliations

  1. Department of Andrology, Urological and Reconstructive Surgery, Mater Misericordiae University Hospital, Eccles. St. 7, Dublin 7, Republic of Ireland

    Fardod O’Kelly MD, Dara Lundon PhD & Paul K. Hegarty MD

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  1. Fardod O’Kelly MD
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  2. Dara Lundon PhD
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  3. Paul K. Hegarty MD
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Correspondence to Paul K. Hegarty MD .

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Editors and Affiliations

  1. Department of Oncology, Mayo Clinic, Division of Medical Oncology, Rochester, Minnesota, USA

    Lance Pagliaro

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O’Kelly, F., Lundon, D., Hegarty, P.K. (2016). Extramammary Paget’s Disease. In: Pagliaro, L. (eds) Rare Genitourinary Tumors. Springer, Cham. https://doi.org/10.1007/978-3-319-30046-7_21

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  • DOI: https://doi.org/10.1007/978-3-319-30046-7_21

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